From parent levels

ChapterIVEndocrine, nutritional and metabolic diseasesOpen

Note

All neoplasms, whether functionally active or not, are classified in Chapter II. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used, if desired, as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.

Exclusions

  • complications of pregnancy, childbirth and the puerperium (O00-O99)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R99)
  • transitory endocrine and metabolic disorders specific to fetus and newborn (P70-P74)
BlockE70-E90Metabolic disordersOpen

Exclusions

  • androgen resistance syndrome (E34.5)
  • congenital adrenal hyperplasia (E25.0)
  • Ehlers-Danlos syndrome (Q79.6)
  • haemolytic anaemias due to enzyme disorders (D55.-)
  • Marfan syndrome (Q87.4)
  • 5-alpha-reductase deficiency (E29.1)
CategoryE72Other disorders of amino-acid metabolismOpen

Exclusions

  • abnormal findings without manifest disease (R70-R89)
  • disorders of: aromatic amino-acid metabolism (E70.-)
  • disorders of: branched-chain amino-acid metabolism (E71.0, E71.1, E71.2)
  • disorders of: fatty-acid metabolism (E71.3)
  • disorders of: purine and pyrimidine metabolism (E79.-)
  • gout (M10.-)

Disorders of sulfur-bearing amino-acid metabolism

Inclusions

  • Cystathioninuria
  • Homocystinuria
  • Methioninaemia
  • Sulfite oxidase deficiency

Exclusions

  • transcobalamin II deficiency (D51.2)
Parent: E72 Other disorders of amino-acid metabolism