ICD-10 / XVII Congenital malformations, deformations and chromosomal abnormalities / Q80-Q89 Other congenital malformations / Q82 Other congenital malformations of skin / Q82.1 Xeroderma pigmentosumFrom parent levelsChapterXVIICongenital malformations, deformations and chromosomal abnormalitiesOpenExclusionsinborn errors of metabolism (E70-E90)BlockQ80-Q89Other congenital malformationsOpenCategoryQ82Other congenital malformations of skinOpenExclusionsacrodermatitis enteropathica (E83.2)congenital erythropoietic porphyria (E80.0)pilonidal cyst or sinus (L05.-)Sturge-Weber(-Dimitri) syndrome (Q85.8)Q82.1CategoryBlock Q80-Q89Chapter XVIIXeroderma pigmentosum